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Table 1 Incidence, prevelance and other statistics for five cardiomyopathies and a more prevalent pediatric congential heart disease called Tetralogy of Fallot or ToF, with associated right ventricular abnormalities.

From: cMRI-BED: A novel informatics framework for cardiac MRI biomarker extraction and discovery applied to pediatric cardiomyopathy classification

CM Subtypes HCM DCM ARVC/D NCM RCM & Iron mediated CM ToF16
Incidence (I) OR Prevalence (P) P = 1:500 in absence of aortic valve disease or systemic hypertension I = 5-8 cases /100,000
P = 36 cases /100,000
I = 1/ 10,000 I = 0.05% to 0.24% I = 11.4% to 15.1% in Thalassemia major patients
Transfusion Dependent
I = 9/1000 live births
#Patients evaluated for CM 46 129 44 31 35 684
Total number of positive diagnosis w/ CMRI CM 11 18 4 15 12 119
cMRI-based QUANTITATIVE markers
LV myocardial wall thickness ABNL ABNL NL ABNL ABNL NL
LV mass index ABNL ABNL NL ABNL ABNL NL
LV Volume index ABNL ABNL NL ABNL ABNL ABNL
RV Volume index NL ABNL ABNL NL ABNL ABNL
cMRI-based QUALITATIVE markers
Myocardial Delayed Enhancement +/- +/- +/- +/- +/- +
Wall motion abnormalities +/- +/- +/- +/- +/- +/-
  1. Some examples of standard quantitative and qualitative markers from cMRI that are associated with observed normal (NL) or abnormal (ABNL) values in each disease based on patients seen at the Children's Hospital of Pittsburgh (CHP) between 2000 and 2013. LV refers to Left Ventricular and RV to Right Ventricular regions. The qualitative variables shown in the table are assigned values of + or - indicating that some patients for the particular subtype indicated presence or absence of that abnormality.